Fibromuscular dysplasia (FMD) was first observed in by Leadbetter and Burkland Intimal fibroplasia (renal FMD). Figure 1: Fibromuscular dysplasia of the right renal artery. The classic “beads on a string” appearance is typical of multifocal fibromuscular dysplasia, the most. Tratamiento de hipertensión vasculorrenal por displasia fibromuscular de is the technique of choice in cases of renal artery fibromuscular dysplasia; but there .

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The value of treatment has not been established for renal artery FMD without hypertension. FMD affecting the arteries of the head neck are commonly recognized as a cause of childhood strokes.

Orphanet J Rare Dis. In the postoperative imaging study renal MRA Figure 2normal kidney fibromusculae was observed with new vascularisation. The gold standard for diagnosing FMD is catheter angiography, but this invasive procedure is only used for patients in whom it is clinically pertinent to proceed with revascularization during the same procedure. Progression of renal artery fibromuscular dysplasia in 42 patients as seen on angiography.

Radiologic findings in a year-old female patient presenting with non-specific headaches. Published online Jun 7. Flow chart illustrating imaging algorithms in case of suspected DFM for both the renal or cervico-encephalic level.

Symptoms may include headaches, insomniafatigue and chest or abdominal pain. Tweet MS, et al. Multi-focal, fjbromuscular, and adventitial; referring to the particular layer of arterial wall being affected.

Fibromuscular dysplasia: a differential diagnosis of vasculitis

The sign is caused by areas of relative stenoses alternating with small aneurysms. Of the later, the discovery of several aneurysmatic dilations displasiq to 1 cm on visceral angiography is considered sufficient for the diagnosis of PAN, even in the absence of histological evidence of the disease, which leads to confusion with FMD.


Even in cases of non-significant renal artery stenosis, the progression of the lesions ought to be monitored. Ipsilateral renal autotransplantation was performed at the right iliac fossa by extraction of the graft with ex-vivo pedicle fbiromuscular, and repair of main trunk and secondary branch of right renal artery and subsequent renal autotransplantation with internal iliac artery and aneurysmorrhaphy.

Inheritance of arterial lesions in renal fibromuscular dysplasia. FMD of the carotid or vertebral arteries can lead to a tear in the artery. Of such conditions, FMD stands out, because it can be a diagnostic challenge, and, when missed, determines inadequate management.

Fibromuscular dysplasia – Wikipedia

Cerebral infarction attributable to cerebrovascular fibromuscular dysplasia. It is governed by the peer review system and all original papers are subject to internal assessment and external reviews.

Introduction Fibromuscular dysplasia FMD is fibromuschlar idiopathic, segmentary, non-inflammatory and non-atherosclerotic disease that can affect all layers of both small- and medium-calibre arteries. Ann Vasc Surg ;23 6: Spontaneous renal artery dissections are rare but frequently coexist with FMD [ 1718 ].

The etiology of FMD remains unknown, despite many theories. Genetic factors The occurrence of renal FMD in ernal pairs or identical twins [ 31 ] suggests its possible inheritability.

Fibromuscular Dysplasia (FMD)

The most frequent locations are the following: Cervico-encephalic arteries The advent of multi-detector CT and the increase in awareness among physicians about the cervico-encephalic location of FMD have certainly participated in increasing the its prevalence. The importance of its diagnosis is mainly due to the fact that it is a potentially curable form of hypertension with stenosis correction.

Seventy ml of Omnipaque is used. The arteries may also become narrow stenosis. In this case, there is severe narrowing of the artery, and the patient was treated with balloon angioplasty.

Rheumatologists should be aware of this differential diagnosis. Author information Article notes Copyright and License information Disclaimer. Blood pressure and renal outcomes in patients with kidney infarction and hypertension.


All authors participated in the drafting and editing of this manuscript and have seen and approved the final version. FMD is currently defined as an idiopathic, segmental, non-inflammatory and non-atherosclerotic disease visplasia the musculature of arterial walls, leading to stenosis of small and medium-sized arteries.

The diwplasia accurate diagnosis comes from combining dispkasia presentation and rena imaging. While the cause of FMD remains unclear, current theory suggest that there may be a genetic predisposition as case reports have identified clusters of the disease and prevalence among twins. A careful prospective multicenter comparative study found that computed tomographic angiography and gadolinium-enhanced magnetic resonance angiography had reasonably good specificities for detecting renal artery stenosis due to FMD 92 and 84 percent, respectively but disappointing sensitivities 64 and 62 percent, respectively [ 38 ].

The therapeutic options for securing ruptured intracerebral aneurysms are microvascular neurosurgical clipping and endovascular coiling. As for cervico-encephalic FMD, the symptoms are not specific. Natural history and prognosis Renal artery FMD, mainly of focal or tubular types, may progress to more severe stenosis and rarely to renal artery occlusion [ 3745 – 47 ].

In vasculitis, vascular stenosis might occur, causing ischemia of the organ or blood vessel displadia, and resulting in aneurysm formation or hemorrhage. The three types are not mutually exclusive. The blood test showed haemoglobin: Computed tomographic angiography and magnetic resonance angiography are probably more effective than ultrasonography for detecting lesions of the middle and distal portions of the carotid and vertebral arteries and may also document or rule out the association of intracranial aneurysms.